AbstractWe present a 45 year nonsmoker male presenting to the Cardiology OPD of AIIMS, Bhubaneswar presenting with effort dyspnea NYHA class IV with features of right heart failure with massive edema of both feet diagnosed to be Cor Pulmonale outside, EKG revealed typical epsilon wave in leads V1 to V3 and echo revealed fibrofatty infiltration of RV apex with reduced RV ejection fraction (35%), Cardiac MRI revealed the same and withdrawing all anti PAH drugs the patient was put on antifailure medications presently doing well. Being a rare entity arrythmogenic right ventricular cardiomyopathy (ARVC) stands out a prominent entity in young RV failure.