Paraneoplastic syndrome occurs as a consequence of tumor in the body, is not due to local presence of tumor but is due to humoral response released by tumor cells or by an immune response against the tumor. It commonly arises from tumor of lung, breast, ovaries and lymphatic system. A 25 year married female with no gynaecological symptoms came with complaints of involuntary jerky movements of both eyes with weakness and numbness in bilateral upper and lower limbs and instability in gait since 1 week. She had fever 3 months back. Initially considered post viral demyelinating disease. Symptoms worsened and in suspicion of Opsoclonus- Myoclonus- Ataxia syndrome, imaging studies and tumor markers done to rule out any tumors in the body. USG showed left adnexal mass which was confirmed on PET scan to have hot spots. Left salpingo-oophorectomy done which on HPE showed benign ovarian teratoma. Post operatively she improved symptomatically.