Background: Ectodermal Dysplasia is a rare disorder. The otolaryngological manifestations range from chronic upper respiratory tract infection to more severe infections of the para nasal sinuses including nasal myiasis. Purpose: The present report describes the rare occurrence of palatal perforation in a case of ectodermal dysplasia, leading to difficulty in feeding and regurgitation. Conclusion: Early detection and addressal of otolaryngologicalproblems associated with ectodermal dysplasia is suggested, so that complications like palatal perforations do not occur.

Keywords: Ectodermal Dysplasia; Otolaryngological Manifestations; Nasal Myiasis Palatal Perforation.