AbstractGoldenhar syndrome also known as Facioauriculovertebral sequence is a rare congenital condition presenting with the asymmetry of the face, underdeveloped ear, cleft lip/palate and abnormalities of the spine. In addition, Goldenhar can affect the heart, kidney, lungs and limb abnormalities. We would like to share one such case presented to us with a constellation of features of Goldenhar syndrome along with a contralateral radial club hand.